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ISSN (Print) 1013-9052
EISSN 1658-3558
The Saudi Dental Journal,
P.O. Box 52500,
Riyadh 11563,
Kingdom of Saudi Arabia
Tel.
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966-1-467-7328
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Fax.
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933-1-467-7308 /
966-1-467-7534
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Email
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saudidj@ksu.edu.sa
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SDJ
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Neurofibromatosis of the maxillofacial region
Khalid A. Al-Ruhaimi, BDS, MSc, Dr Med Dent*
Hermann F. Sailer, Dr Med, Dr Med Dent**
*Oral and Maxillofacial Surgery, Department of Biomedical Dental SciencesCollege of Dentistry, King Saud University
**Oral and Maxillofacial Surgery, Zurich University Hospital & Dental School, Zurich
In this study seventeen patients with neurofibromatosis in the maxillofacial region were presented. There was no great difference in the incidence of the disease between males and females. The patient age range was 1 to 75 years with a mean age of 21.5 years. Family history was positive in 5 cases. The spectrum of the clinical manifestations of this disease, known for its protean characteristics, were evident in all of our 17 patients. 14 (82.4%) patients had cafe'au-lait spots; 3 (1 7.6%) had multiple cutaneous nodules; malignant transformation was documented in only one case (5.9%). Psychologic depression was recorded in 2 (11.8%leases, and one(5.9%) case had grand-mal epilepsy. A rare location of neurofibromatous nodules, i.e. in eye (iris nodules), was reported in only one (5.9%) case. The most frequently performed procedure in our cases was excision of the tumor mass which was, in most instances, incomplete. However, massive bleeding during surgical intervention was prominent in four cases and was overcome with extensive packing removed after approximately two weeks. An interesting finding in this study was the incidence of radiologic findings which was higher (76.4%) than previously reported. All cases of this study were unilateral and involvement of the mandible (65%) was more than that of the maxillae.
Saudi Dental Journal 1989;1(1):2-7.
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